Primary retroperitoneal tumors are a rare entity of human neoplasms, with primary retroperitoneal neuroendocrine tumors being even more rare. They are usually metastatic and rarely seen as a primary tumor. We report a case of primary retroperitoneal neuroendocrine tumor in a 55-year-old lady, who presented with chronic abdominal pain. Computed tomography showed a retroperitoneal mass and biopsy confirmed the diagnosis of primary retroperitoneal neuroendocrine tumor. Primary retroperitoneal neuroendocrine tumors are rare tumors. Radiology plays a crucial part in the diagnosis of such tumors with the CT scan considers the best imaging modality for diagnosis. Surgical resection remains the definite treatment of retroperitoneal neuroendocrine tumors. Chemotherapy is used for unresectable differentiated tumors.

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