In this report, we described two male patients with Hughes-Stovin syndrome. The first patient was a 26-year-old male who initially presented with deep vein thrombosis (DVT) in the right lower limb followed shortly by hemoptysis. Pulmonary CT angiography revealed bilateral pulmonary artery aneurysms secondary to underlying pulmonary vasculitis. While the second case was a 16-year-old male patient who initially presented with generalized fits due to sagittal sinus thrombosis and later followed by DVT in the left lower limb. Pulmonary CT angiography showed small pulmonary artery aneurysms with thrombosis of peripheral pulmonary artery branches. Both patients were treated successfully with steroids and immunosuppressive therapy and showed clinical improvement.

A case of Hughes-Stovin syndrome (incomplete Behçet's disease) with extensive arterial involvement Unmasking the true face of a rare syndrome Robinson et al. [16] Case 4: A 21-year-old male; recurrent oral ulcers; no genital ulceration; superficial thrombophlebitis; pulmonary CT angiography a 35 mm right lateral segmental PAA with multiple pulmonary artery in situ thromboses Demirkan and Gültekin [17] Case 5, 6: two patients with HSS who presented with pulmonary artery aneurysm, thrombophlebitis, hemoptysis, and oral ulcers Al-Jahdali [18] Case 7: 23-year-old Saudi woman; recurrent oral ulceration; right-lower lobe PAA; papilledema; DVT Yagi et al. [19] Case 8: A 32-year-old male; multiple PAA; DVT of the right leg and the right femoral vein; thrombosis of the vena cava; aphthous ulcer in the oral cavity, an ulcer in the genital region Madiha and Sami [20] Case 9: DVT; oral ulcers; giant aneurysm in the left lower lobe pulmonary artery Summary of HSS case reports without features of the classic triad of BD Hughes and Stovin [1] Case 1, 2: two male patients; segmental PPA with peripheral venous thrombosis Kopp and Green [21] Case 3, 4: two male patients; PAA and recurrent thrombophlebitis Fabi et al. [22] Case 5: A 12-year-old boy; right atrium endocardial mass; jugular vein and cerebral venous thrombosis; deep venous thromboses; PAA Abdelbary et al. [23] Case 6: A 35-year-old Egyptian female lower limb deep vein thrombosis; pulmonary aneurysm Ribeiro et al. [24] Case 7: A 43-year-old male; superficial thrombophlebitis and DVT of the lower limbs; PAA Pankl et al. [25] Case 8: A 41-year-old man; deep venous thrombosis of the right leg, and PAA Al-Zeedy et al. [26] Case 9: A 53-year-old man; DVT and PAA Kably and Reveron [27] Case 10: A 41-year-old male; massive hemoptysis; ruptured PAA; DVT; cardio-venous thromboembolism; pulmonary infarction El Aoud et al. [28] Case 11: A 42-year-old woman; DVT; PAA Jaramillo et al. [29] Case 12: A 47-year-old male; dilated main pulmonary arteries, multiple right bronchial artery aneurysms and a splenic artery aneurysm Silva et al. [30] Case 13: A 25-year-old male; DVT; PAA Grembiale et al. [31] Case 14: DVT; PAA; Budd-Chiari syndrome; a thrombotic occlusion of inferior vena cava Amezyane et al. [32] Case 15: A 28-year-old female; right ventricular thrombus, PAA, iliac vein thrombosis; caval thrombosis Kim et al. [7] Case 16: A 45-year-old man; massive hemoptysis; DVT; bilateral PAA and inferior vena caval thrombosis Chalazonitis et al. [9] Case 17: A 18-year-old, Greek male patient; DVT; PAA; superior sagittal and transverse sinuses Emad et al. [2] Case 18, 19: two male patients; DVT, PAA, superior sagittal sinus thrombosis in one case Balci et al. [33] Case 20: A 41-year-old patient; multiple PAA; thrombus in both the inferior and superior vena cavae Herb et al. [34] Case 21: A 25-year-old man; PAA; multiple aneurysms of the bronchial arteries; severe hemoptysis; aneurysm of the left hepatic artery Margolesky et al. [35] Case 22: A 38-year-old woman; DVT, PAA; right ventricle th...

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Pulmonary vasculitis complicating ulcerative colitisLong-standing ulcerative colitis complicated by right subclavian artery occlusion and upper limbs arteriolitis with digital ischemia Abstract A 48-year-old male patient with long-standing ulcerative colitis since February 2001 which was diagnosed by endoscopy, developed acute digital ischemia affecting both hands with fixed colour changes in the left index finger which was followed shortly by digital ulceration. Magnetic resonance angiography (MRA) of both upper limbs showed evidence of vasculitis affecting digital arterioles on both sided and right subclavian occlusion. The patient received pulse methylprednisolone followed by cyclophosphamide pulse therapy, the latter continuing on a monthly basis for 6 months with appreciable improvement and remission of the vasculitic process; follow-up MRA showed reperfusion of the previously occluded subcalvian artery. To the authors' knowledge vasculitis complicating the course of ulcerative colitis is a rare association and is only sporadically reported in the literature. This rare entity should be diagnosed early and aggressively treated; MRA is a very promising diagnostic tool that is suitable for both diagnosis and follow-up of patients with this rare entity.