Moyamoya disease is an angiogenic disorder and a rare cause of stroke, it is a progress narrowing of cerebral arteries at the base of the brain involving the intracerebral portion of the internal carotid arteries, where it leads to development of collateral arteries, causing a "cigarette smoke" aspect. We report a case of 9 years old male child who was admitted in our institution with the complaint of vomiting, weakness over the right upper and lower limb, facial palsy and speech disturbances. On C.T, angiography the child was diagnosed to have moyamoya disease. KEYWORD: Moyamoya disease, right hemiplegia, facial palsy, MRI, C.T. Angiography. INTRODUCTION: Moyamoya (A Japanese term) meaning hazy things such as puff of smoke and was first described by Takeuchi and Shimizu in 1957 {2, 4, 5} the over all incidence is higher (0.35 per 1,00,00) Takeuchi was distinguished two forms of this disease as primary moyamoya disease and secondary moyamoya disease. Moyamoya disease is a rare cerebrovascular disease of known aetiology {1} we reported a case of 9 years old male child who presented with right hemiplegia, Facial Palsy and disturbed speech at Owaisi hospital and research centre attached to Deccan College of Medical Sciences Hyderabad, A.P. India. CASE REPORT: A 9 years old male child was admitted in our institution with a complaints of loose motion and vomiting, the child was initially treated as acute gastroenteritis. Three days later the child developed sudden onset of weakness over right upper & right lower limb, and deviation of the mouth to the left side. Over a period of 1 week, the child was developed altered Sensorium and slurred speech. There was history of convulsion at the age of 4 years for which, the child was treated as a case of febrile convulsion. There was no history of fever, head injury and delayed milestone. On neurological examination right facial palsy was detected, gait was hemiplegic, tone was decreased over right side. Power was 2/5 over right upper and right lower limb, deep tendon reflexes was exaggerated, and planter was extensor over right side. No signs of meningeal irritation. CSF examination was normal.
