ObjectivesTo report an unusual presentation of a Lobular Capillary Hemangioma in a 48 h old neonate to inform practitioners on the importance of proper identification of the lesion, differential diagnosis and management.Case presentationWe report the case of a newborn female presenting with a pedunculated mass on the right hand, port-wine colored that quickly turned dark purple indicating thrombosis. The mass was surgically excised without complications and histopathology analysis reported a LCH. An abdominal and renal ultrasound was requested to rule out any underlying abnormalities. At follow-up, two months later, there is adequate healing and no related complications.ConclusionsLobular Capillary Hemangioma is a rare vascular malformation that occurs at an early age in the head and neck in most cases. We report an unusual case of a newborn female patient with a pedunculated lobular hemangioma on the right hand. Surgical treatment was performed with good cosmetic results. Our case is relevant as it raises awareness of the different diagnoses a congenital mass can be and that we, as physicians, should take into consideration when making a diagnosis and treatment.