Odontodysplasia is a rare nonhereditary developmental anomaly of dental hard tissue with unknown etiology, arising from both ectodermal and mesodermal components. Hitchin in 1934 first described it as a localized arrest of tooth development generally affecting one quadrant of the jaw. When it just affects one quadrant, it is referred to as “regional odontodysplasia,” but when it crosses the midline and affects more than one quadrant, it is referred to as “generalised odontodysplasia.” In this two case series, various types of odontodysplasia have been described, one of which is confined to a single quadrant and the other crossing the midline. The cases of odontodysplasia can only be treated by multidisciplinary approach and restorative and prosthetic rehabilitation and regular follow-up require for improving the quality of life of patients.

Ectrodactyly–ectodermal dysplasia–clefting (EEC) syndrome is a rare hereditary congenital defect characterized by a triad of disorders such as ectodermal dysplasia, malformed extremities, and cleft lip and/or palate. We report the case of a 3-month-old girl child with clinical signs of EEC syndrome and offer valuable information into current knowledge about this syndrome. The symptoms of EEC display diversity in both extension and expression. Early diagnosis and management of clinical manifestations associated with this syndrome presents a unique challenge due to the paucity of documents in the literature.

Mucocele is one of the most common minor salivary gland disorders which can arise due to the accumulation of mucous secretion due to trauma or any aberrant oral habit. Primarily of two types – extravasation and retention type based on histopathological features. Mucocele can appear at any site in oral cavity in association with minor salivary glands such as lip, cheeks, and the floor of the mouth but most commonly found in lower lip. It can affect patients of any age group but young population are most frequently affected. Mucocele is usually diagnosed based on its clinical findings. Surgical removal is the most common treatment of choice.

Preterm births are which occur prior to 37 weeks gestation and in developed Western nations it comprise approximately 6 per cent of all live births. Along with having many serious medical problems, it has been hypothesized that the development of oral tissues may get affected in the neonatal period. In preterm children, a high prevalence (around 40-70%) of generalized enamel hypoplasia had been found in previous studies in the primary dentition and it is plausible to be associated with low bone mineral stores. Other than enamel hypoplasia, crown dilacerations, and palatal distortions are other defects that are frequently observed in preterm children which are usually associated with traumatic laryngoscopy and prolonged endotracheal intubation. The incidence of ECC (International Caries Detection and Assessment System: ICDAS ≥ 2) was also found to be high in low birth weight children. The etiology behind this is multifactorial but maternal factors, maternal factors might play the role of contributing factors. The current review would analyse the dental anomalies in preterm children in depth which might have significant implications in monitoring possible anomalies and in treatment intervention can be done at an early stage. Key words: Premature birth, Very low birth weight, Dental defects, Enamel hypoplasia.

Hypertelorism-microtia-clefting (HMC) syndrome is a very rare autosomal recessive disorder. HMC syndrome is malformation of orofacial region characterized by hypertelorism, microtia, and cleft lip and palate. Additional features such as microcephaly, congenital heart disease, and kidney abnormalities can also be present in HMC syndrome. Only few case reports of this syndrome have been documented in dental literature. In the article, we report a case of 9-month-old girl child presenting with typical features of this syndrome. The rarity of the syndrome prompted us to report the case.