Introduction: This article discusses about our case of cleidocranial dysplasia and a review for dental manifestation and management of these cases. This disorder has a genetic background and general manifestations of CCD are outlined and an overview is presented. History: CCD is one of the best studies and documented disease whose history dates back to the prehistoric times with first case documented by Greig in 1933 in the museum of royal college of surgeons in Edinburgh. In the year of 1871, Scheuthauer published cranial and non – cranial findings of CCD. Case Report: We present a case of a 17 year old male patient who reported to our hospital with a complain of smaller and yellowish discolored teeth with spacing in the arch causing difficulty in chewing food. We have documented this case to the best of our understanding and with pictures depicting the patient and his clinical and radiographic findings. An interesting overview of the patient has been described. Discussion: We have researched different articles related to our patient and have documented the prominent features seen in these patients and correlated with the findings in our patient. There are reports of multiple patients who were diagnosed at a much earlier stage than our patient. Most of the clinical features described in the previous literature coincide with other findings, however additional clinical findings have been mentioned irrespective of their presence in our patient or not. Conclusion: We conclude that a proper clinical and radiographic evaluation can lead to early diagnosis of these patients and hence can aid in their management and education of the patient and his care takers. There are no reported cases of deficient IQ or abnormal life experienced by these patients except for that related to short stature.