Darier's disease is an autosomal dominant disorder characterized clinically by presence of keratotic papules in a seborrheic distribution, nail involvement and mucosal lesions. There are several clinical variants of Darier's disease, but few cases of segmental Darier's disease have been described in the literature. We describe a 12year old boy with type 2 mosaic phenotype. This unique clinical variant of Darier's disease has been described very rarely.

Episcleritis refers to inammation of the loose connective tissue between the sclera and the conjunctiva. The majority of episcleritis cases are idiopathic, but 26% to 36% of patients have an associated systemic disorder that is responsible for the pathological process and development of episcleritis. It is also well established that the incidence and prevalence of episcleritis are higher in populations with systemic collagen-vascular disease and autoimmune diseases. However recurrent episcleritis in Mixed Connective Tissue Disease has not been reported before in literature Here we are reporting a case of recurrent bilateral nodular episcleritis as a rare presentation of MCTD.