BACKGROUND Paediatric retinal diseases are very different from adults, presentation is unique compared to adults, various hereditary and acquired causes of retinal disorders are discussed in our study. Though we have significantly advanced techniques to diagnose, still management of these cases is really challenging to vitreo retinal surgeons. We wanted to study various causes of retinal diseases seen in the paediatric population at a tertiary eye hospital in Telangana state. METHODS All paediatric cases presented to vitreo-retinal department of Sarojini Devi Eye Hospital were studied in detail from electronic medical records to know the various retinal diseases in children. Retrospective study was done. Patients of different age groups who presented from paediatric ophthalmology dept. for indirect ophthalmoscopy were examined in detail. Data of patients who presented to vitreoretinal dept. during June 2016 to June 2018 were collected from the records. All patients underwent detailed ocular and systemic examination, and management was done based on the clinical presentation. 120 patients were referred during the two-year period from paediatric ophthalmology department to retina dept.; age range was between 2 to 15 years; mean age of presentation was 9 years, most of the patients were male. RESULTS All 120 patients were examined in detail and treated based on the clinical presentation, many conditions were congenital; acquired causes were also noted. Results were not favourable due to delayed presentation. CONCLUSIONS Early detection of low vision in children helps to prevent blindness. Regular and frequent screening programmes at schools also help in preventing blindness in children.