Venous malformations (VMs) are dyssembryogenias of the venous vascular system. Giant VMs are rare but frequently associated with hemostasis disorders of variable severity. Their treatment is long and complex. The combination of several therapeutic modalities can reduce symptoms without eliminating the VM. A multidisciplinary approach is essential. A clinical case illustrates the difficulty of managing these malformations.

Juvenile aponeurotic fibroma is a rare benign tumor which occurs in young patients and found primarily in the extremities. Clinical presentation is a unique, hard and painless tumour of the palm or sole which has a strong propensity to recur. The treatment commonly accepted for this locally recurrent tumour is complete excision with function preservation. With a close supervision to identify any recurrence or development of metastases at early stages.

Congenital tumors of the oral cavity are infrequent and is dominated by teratogenic tumors. They are rarely associated with cleft palate. Congenital lipoma of the palate in patients with cleft palate remains exceptional. We report a case of congenital septal lipoma with cleft palate (the third case of such association is reported in the literature) and discuss the surgical treatment in light of the evolution of the patient.