A 24-year-old primigravida with monochorionic monoamniotic pregnancy presented to our institution at 31+3 weeks of gestation with leaking per vaginum. The ultrasound findings were that of an enlarged and cystically dilated placenta, which raised the possibility of a differential diagnosis of partial mole. In view of foetal distress she was taken up for emergency caesarean section. Two healthy female twins were delivered with no features of Beckwith Wiedermann syndrome.On gross examination the placenta weighed 800 gm and measured 17x15x2.5cm. The two umbilical cords attached measured 20cm and 24cm respectively [Table/ Fig-1]. Foetal surface showed prominent, dilated blood vessels. The maternal surface was intact with cotyledons. Tiny, white nodules were seen on the foetal side. The cut surface of the placenta was beefy red with no pale areas. A focal area showed pinkish white vesicle like area [Table/ Fig-2].

Malignant gastrointestinal neuroectodermal tumor (GNET) is a rare neoplasm with unknown etiology. It was previously referred to as Clear cell sarcoma of gastrointestinal tract. This tumor is characterized by a higher rate of local recurrence and metastasis. Due to its aggressive clinical course, distinguishing this entity from various other mimickers is very essential. Herein, we present a case of malignant GNET in a 33-year-old male patient.