Neurofibromatosis type 1 is a multisystem genetic disease of autosomal dominant transmission that reveals important cutaneous manifestations such as café-au-lait spots, multiple neurofibromas, and ephelides in skin fold areas, as well as hamartomatous lesions in the eyes, bones, glands, and central nervous system. Moyamoya disease is a rare progressive vaso-occlusive disorder that occurs with important ischemic cerebrovascular events. Despite the rarity of this association in childhood, children diagnosed with neurofibromatosis type 1 and focal neurologic symptoms should be investigated for moyamoya syndrome. The present study reports the case of a pediatric patient with a rapidly progressive cerebrovascular accident and a late diagnosis of Neurofibromatosis type 1 associated with moyamoya disease.

Leprosy is a chronic infectious disease caused by Mycobacterium leprae, which affects peripheral nerves, skin and mucous membranes. The impairment of neural function as well as sensory or sensory-motor disabilities in leprosy continue to be a problem that requires careful attention in the management of patients with the aim to avoid or minimize their progression to prevent sequelae. One of the most common characteristics of these ulcers is the tendency to chronicity, with variable therapeutic response. In this article, we shall discuss the therapeutic management of thirteen trophic leprosy ulcers in eight patients using polyhexanide 0.2% products.

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A realização de procedimentos cirúrgicos na Unidade Básica de Saúde é preconizada e descrita na literatura. No entanto, tal prática vem sendo cada vez menos aplicada na atenção primária. Em um contexto de superlotações de hospitais terciários e consequente inoperação de cirurgias eletivas, é de extrema importância a realização desses procedimentos na Clínica da Família. Nesse trabalho, apresenta-se um caso de um paciente submetido à exérese de lipoma gigante incapacitante, na fossa poplítea esquerda, com 12 anos de evolução e com tentativa frustrada de resolução cirúrgica em um hospital terciário.