Primary ciliary dyskinesia is a rare, autosomal recessive disease, with diminished ciliary motility resulting in chronic disease of the upper and lower airway. Due to its low prevalence, there are few studies with significant numbers of cases, and a lack of guidelines for the management of this group of patients. Most patients present chronic rhinosinusitis at diagnosis and while there is improvement with saline irrigations and medical treatment, its effects are increased after endoscopic sinus surgery. Despite this improvement, the high risk of early recurrence, forces us to reserve it for cases with severe nasal obstruction. The aim of this study is to present a literature review on this topic.

Two patients who had squamous cell carcinomas of the nasal cavity with extension to the nasal septum and previous treatments with surgery and in another with surgery and radiotherapy were treated by rhinectomy.The reconstruction of the internal mucosal lining was done with mucoperiosteal flaps from the lateral nasal wall with anterior pedicle with the assistance of endoscopes.There are few descriptions in the literature of the use of this flap to reconstruct the inner lining after rhinectomy.