The management of severe laparoschisis is a big challenge in health facilities with limited technical capabilities. Unfortunately up to date, there is little data/research on this concern in Congolese medical practice and the etiology is still unclear. The case we report was born from vaginal delivery at the health center and then was referred to the referral hospital for adequate care, as the management was not appropriate, it was later aggravated by symptoms of sepsis and resulted in death. An appropriate management of such a case requires a total and frank collaboration between the health care’s providers and patients relatives. It also raises a need for further research toward appropriate management, not to mention preventive interventions.