Objective-To determine in pediatric Duchenne (DMD) and Becker (BMD) muscular dystrophy or other dilated cardiomyopathies (ODCM) whether outcomes differ by diagnosis.Background-Children with dilated cardiomyopathy are treated as a single undifferentiated group.

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Even in this homogeneous LQTS population, the phenotype was so variable that clinical and detailed ECG analyses did not permit an accurate diagnosis of gene carrier status, especially in children. Sustained microvolt TWA was a specific (100%) but insensitive (18%) marker for LQTS. Its ability to predict risk of arrhythmia in this population remains to be determined. Genetic testing serves an essential role in screening for carriers of LQTS.