Background Hemophilia B is an X-linked inherited disease, mainly caused by deficiency of factor IX. Severity of the disease is manifested by the factor IX deficiency in the blood. Case presentation This paper presents our experience in the cochlear implantation with hemophilia B in an 11-month child with profound sensorineural hearing loss. The patient had normal hematological parameters pre-operatively and surgery was uneventful. After 36 h of the surgery, the patient developed right periorbital ecchymosis, extending to the left eye with a soakage of bandage. With timely early intervention, the bleeding stopped and ecchymosis was resolved. Conclusion To our knowledge, cochlear implantation in hemophilia B has not been reported previously. Cochlear implantation can be safely done in hemophilia A and B with timely correction of deficient factors.

No abstract