The radiographic findings in 25 patients with the nevoid basal cell carcinoma syndrome are presented. Cystlike lucencies of the phalanges, a previously unreported finding, were seen in 46% of the patients in whom hand films were obtained. Mandibular cysts, present in 42% of cases, and exuberant intracranial calcifications were also characteristic features. Brachymetacarpalia, and rib and spine anomalies were also associated with the syndrome but are less specific findings.
Hepatic bile duct cysts were demonstrated on an abdominal CT scan and confirmed at autopsy in a patient with polyarteritis nodosa. The cysts developed in close proximity to hepatic artery aneurysms and occlusions visualized at hepatic arteriography and confirmed postmortem. The development of similar bile duct cysts following hepatic artery occlusion was demonstrated in 13 Rhesus monkeys.
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