We report on the association of aplasia cutis congenita (ACC) in the midline of the scalp vertex and coarctation of the aorta (CA) in mother and son. The acronym of ACCCA syndrome is proposed for this condition. Autosomal dominant inheritance is most commonly implicated in the familial cases of ACC. The familial aggregation of CA is attributed, in general, to a multi-factorial causation, with a few reported families suggesting autosomal dominant inheritance. The ACCCA syndrome could be due to a Mendelian mutation.

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Dr. Senturia, a well-known authority on diseases of the external ear, has provided a text which promises a better understanding of the diseases of the external ear. The book comprises the results of 5 years of co-ordinated laboratory and clinical research in a group of diseases which, although quite common, have not been approached scientifically in the past. The chapter concerned with pathology is profusely illustrated, and of special interest to the practitioner are the chapters on pathogenesis and prophylaxis of external otitis.