A B S T R A C TGanglioneuroma is a rare benign tumor originates from neurol crest and may develop anywhere along the sympathetic nervous system is present. Nearly all patients with ganglioneuroma are older than 10 years old. In most cases ganlioneuromas are detected incidentally during work-up for unrelated conditions. Nevertheless, radiological and differential diagnosis of retroperitoneal masses may be challenging. We present management of a 6-year-old boy with ganglioneuroma that located in left retroperitoneum.