OBJECTIVE
Torcular dural sinus malformations (tDSMs) are rare pediatric cerebrovascular malformations characterized by giant venous lakes localized to the midline confluence of sinuses. Historical clinical outcomes of patients with these lesions were poor, though better prognoses have been reported in the more recent literature. Long-term outcomes in children with tDSMs are uncertain and require further characterization. The goal of this study was to review a cohort of tDSM patients with an emphasis on long-term outcomes and to describe the treatment strategy.
METHODS
This study is a single-center retrospective review of a prospectively maintained data bank including patients referred to and cared for at The Hospital for Sick Children for tDSM from January 1996 to March 2019. Each patient’s clinical, radiological, and demographic information, as well as their mother’s demographic information, was collected for review.
RESULTS
Ten patients with tDSM, with a mean follow-up of 58 months, were included in the study. Diagnoses were made antenatally in 8 patients, and among those cases, 4 families opted for either elective termination (n = 1) or no further care following delivery (n = 3). Of the 6 patients treated, 5 had a favorable long-term neurological outcome, and follow-up imaging demonstrated a decrease or stability in the size of the tDSM over time. Staged embolization was performed in 3 patients, and anticoagulation was utilized in 5 treated patients.
CONCLUSIONS
The authors add to a growing body of literature indicating that clinical outcomes in tDSM may not be as poor as initially perceived. Greater awareness of the lesion’s natural history and pathophysiology, advancing endovascular techniques, and individualized anticoagulation regimens may lead to continued improvement in outcomes.
Background: Pyomyositis is an infectious disease
usually encountered in tropical regions. It typically occurs in
immunocompromised hosts and most commonly affects lower limb muscles. Our
patient was a healthy Canadian with an atypical presentation of cervical
pyomyositis. Methods: We report a case of a healthy
22-year old woman presenting to the emergency department with unprovoked
severe bilateral cervico-occipital pain and nuchal rigidity. She remained
afebrile. Review of the literature was conducted to search for similar
presentations. Results: A Computed Tomography scan of
the head and neck demonstrated the presence of a ring enhancing lesion in
the semispinalis capitis muscle extending from the occiput to the C4 level.
The abscess was surgically drained and cultures grew staphylococcus aureus.
The patient rapidly improved on intravenous antibiotics. Literature review
revealed this to be the first Canadian case of cervical pyomyositis.
Conclusions: Cervical pyomyositis can be
complicated by local destruction of the vertebrae, septic shock,
endocarditis, septic emboli, brain abscess or rhabdomyolysis. Early
diagnosis and source control is necessary to reduce the risk of morbidity.
Therefore, it is important to consider this rare disease in the differential
diagnosis of cervicalgia even in healthy immunocompetent patients.
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