Teratomas are true neoplasms originating from pluripotent cells and are composed of tissues from all three germinal layers, usually benign in nature. The most common sites are the sacrococcyx, anterior mediastinum, testicle, ovary, or retroperitoneum. Teratomas of head and neck are exceedingly rare and only about 10% of teratomas are found in this area. Nasopharynx and cervical region are the most common sites. We describe a one-day old female neonate with a large oral teratoma originating from the tongue which was successfully treated with surgery.