Introduction:Pulmonary artery sling is a rare congenital heart disease in which the LPA is originating from the RPA then encircling the distal trachea and the right main bronchus. 1 This is a malformation that is often revealed while investigating respiratory distress and congenital heart disease in infants. The respiratory signs are not specific and may include wheezing, stridor, dyspnea on effort, coughing and recurrent infections of lower airways. 2 In ideal situation, 3 the diagnosis is made by echocardiogram while the bronchoscopy accesses the bronchial stenosis. The treatment is strictly surgical and classically consists of cutting the LPA then reimplanting it on the pulmonary artery (PA) main stem by sternotomy and cardiopulmonary bypass (CPB). Tracheal repair is indicated if the patient is clinically symptomatic. We report a case of PAS in a 5.5 years old boy diagnosed in the Department of Cardiology of the University Hospital of Fann Dakar then successfully repaired in Monaco. Case report:AD, a boy of 5.5 years old was admitted for dyspnea with stridor occurring on exercise. There was no dizziness, sweating or cyanosis. On the previous medical history, a recurring bronchitis is reported but there was no consanguinity and the pregnancy was followed up to deliverance. He was hospitalized twice at the ages of 2 months old and 3.5 months old respectively for dyspnea and stridor that were treated by salbutamol puff and physiotherapy. The physical examination showed a good growth regarding the weight (21 Kg) and height (121cm) which were corresponding to Z score -0.94. The cardiovascular examination was normal with oxygen saturation at 98%. The respiratory examination showed suprasternal retraction and expiratory wheezing. There were no abnormal findings in the liver, ENT and dental areas. On the chest X rays, cardiac outline, pulmonary