Introduction: idiopathic pulmonary hemosiderosis is a rare disease of unknown etiology. Case report: This is a 12-year-old boy. The beginning of its symptomatology dates back to one year by several episodes of low-abundance hemoptysis associated with cough and night sweats. He had also a microcytic hypochromic anemia (Hb=4.4) transfused 3 times. . Clinical examination found discoloured skin paleness and conjunctival The count showed microcytic hypochromic anemia with HB:5.7 g/dl. A chest x-ray showed a discrete alveolar syndrome. A tuberculous assessment in particular an IDR tuberculin 3 BK expectorations and Gènexpert were negative. A chest CT scan showed bilateral interstitial syndrome. A bronchoscopy with bronchoalveolar lavage showed the existence of sidephages with a Golde score calculated on 240 Perls staining . A balance of system diseases including antinuclear antibodies were negative. Ac anti transglutaminase IgA were negative. A heart ultrasound did not show a pulmonary hypertension. In fine, the diagnosis was a primary pulmonary hemosidesis. Management consisted of a blood cell transfusion a prenisolone-based corticosteroid 2 mg/kg/d for 3 months. After two months, the improvement was full. Conclusion: We must think about Hemosidesis idiopathic if we have hemoptysis chronic anemia and pulmonary infiltrates and do a Bronchoalveolar lavage to confirm diagnosis.
Langerhans cell histiocytosis is a rare clonal disease defined by an accumulation of dendritic cells with Langerhans cell immunological properties within different organs of the body. We intend to describe a new case of Langerhans cell histiocytosis of the temporal bone in a child with central diabetes insipidus. The child presented the polyuria-polydipsia syndrome for 6 months with Chronic bilateral otorrhea. On physical examination,there were bilateral retroauricular redness and induration. The otoscopy visualized inflammatory polyps filling all of the right and left external ear canal. Biological exploration confirmed the central diabetes insipidus. Magnetic resonance imaging of the brain showed the presence of pituitary infiltration. Computed tomography showed osseous lysis of the temporal bone bilaterally. A retroauricular biopsy was performed under general anesthesia. Histological and immunohistochemical evaluation confirmed the diagnosis of Langerhans cell histiocytosis
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