No abstract

No abstract

INTRODUCTION: VACTERL association is not known to be a predisposing factor to malignancy. We present a rare case of carcinoid tumor presenting in a young, man with VACTERL. CASE PRESENTATION: An 18-year-old black male with a history of right-sided hydronephrosis with right nephrectomy at 7months old, clubbed feet, scoliosis and patent VSD presented to SUNY Downstate Medical Center with intermittent hemoptysis for four months. Physical exam demonstrated scoliosis and a grade 3/6 pansystolic murmur. Labs were unremarkable. CT of the chest revealed a 2.3cm right peribronchial mass with an endobronchial component eroding into the bifurcation of the bronchus intermedius. Subsequent bronchoscopy and biopsy of the mass revealed epithelial cells in a chondromyxoid stroma suggestive of a pleomorphic adenoma. Video-Assisted Thorascopic surgery (VATS) and bilobectomy of the right middle and lower lung lobes provided surgical histology, which confirmed the diagnosis of Typical Carcinoid tumor. Somatostatin Receptor Scintigraphy (SRS) showed no evidence of residual tumor or metastases.

No abstract