Background: The aim of the study was to evaluate the role of cardiopulmonary exercise testing (CPET) parameters in assessing exercise capacity improvement after percutaneous pulmonary valve implantation (PPVI (25.3 ± 3.3 to 24.3 ± 3.0, p = 0.04) and oxygen consumption at peak exercise (pVO 2 ) (20.4 ± 5.0 to 22.6 ± 5.3 mL/ /kg/min, p = 0.04). Improved EQCO 2 correlated with an increase in right and left ventricular ejection fraction (respectively R = -0.57, p = 0.002; R = -0.56, p = 0.002). In this study, no baseline factors that might affect improvement in exercise function were found. Conclusions: Successful PPVI leads to an improvement in exercise capacity and hemodynamic response to exercise. The correlation between the improvement in EQCO 2 or peak VO 2 and baseline characteristics was too weak to reliably identify the group of patients that will benefit from the procedure. (Cardiol J 2015; 22, 3: 343-350) Key words: percutaneous pulmonary valve implantation, cardiopulmonary exercise testing, grown up congenital heart disease 343

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A 21 year old woman with phenylketonuria, positive hepatitis B surface antigen and anomalous left coronary artery originating from the pulmonary artery (ALCAPA) was referred to our clinic to asses her current condition and to establish her further treatment. ALCAPA with concomitant mild mitral insufficiency were confirmed. She was asymptomatic and the studies provided evidence for not qualifying her to surgery.