It is unusual for two tumours of completely different origins to occur simultaneously in the same patient. Such an occurrence was described in 1969 when the association of a gastric tumour and a pulmonary hamartochondroma was noted (Vio et al, 1969). In 1977, Carney et al described four patients with co-existing gastric epithelioid leiomyosarcomas (leiomyoblastomas), pulmonary chondromas and functioning extra-adrenal paragangliomas and suggested their occurrence together should constitute a syndrome (Carney et al, 1977; Carney, 1979).
Since 1974, a number of cases have been reported showing some or all of the features of Carney's triad. Most of these patients have presented because of gastric tumours which are in most cases either leiomyoblastomas (Muller et al, 1974; Appelman & Elwig, 1976; Carney et al, 1977; Tisell et al, 1978; Knake & Gross, 1979; Grace et al, 1981; Cuilleret et al, 1984; Mishkin et al, 1985) or leiomyosarcomas (Chander et al, 1981; Dajee et al, 1982; Chahinian et al, 1983). Pulmonary chondromas are the second most common component of the syndrome and paragangliomas the least common, possibly because the latter tend to appear late.
We present a case of a 12-year-old girl with multiple gastric leiomyoblastomas and pulmonary chondromas. So far, after 6 years follow-up, a paraganglioma has not been detected. This patient is an example of an incomplete Carney's triad.
A 12-year-old girl was admitted to hospital in 1980 for investigation of possible pulmonary hydatid disease discovered on routine examination by her GP.
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