The term Scheuthauer-Marie-Sainton syndrome is also known as cleidocranial dysplasia or cleidocranial dystosis and is derived from ancient greek words cleido (collar bone), knanion (head) and dysplasia (abnormal formation). It is an uncommon but well known genetic skeletal condition and an autosomal dominant malformation affecting bones and teeth. The most common skeletal and dental abnormalities in affected individuals are hypoplastic/ aplastic clavicles, open frontanelles, short stature, retention of primary teeth, delayed eruption of permanent teeth, supernumerary teeth and multiple impacted teeth. Affected person have a characteristic facial appearance with a bulky forehead, hypertelorism and midfacial hypoplasia. General health is usually good and the intellect is unimpaired. This article describes clinical and radiographic features of Scheuthauer-Marie-Sainton syndrome in a 29 years old male patient

Odontogenic Keratocyst (OKC) is a clinico-pathologically distinct form of developmental odontogenic cyst. It is known for its aggressive biological behavior and high recurrence rate. Odontogenic keratocyst (OKC) is the third most common odontogenic cyst and comprises about 12% of all the cysts occurring in the maxillofacial region. OKC has a distinct feature to occur in body of the mandible and ramus. But it can also be found in the maxilla especially in the canine region. We present a rare case of OKC in maxillary sinus of a 35 year old female patient which is associated with ectopic third molar that can be easily confused with other lesions of maxillary sinus like sinusitis or antral polyps. Involvement of the maxillary sinus by OKC is rare with < 1% of cases reported in the literature.