Deafblindness is a rare disease in which a person has a combination of hearing loss and vision loss, resulting in reduced access to both auditory and visual information. There are many reasons to occur of deafblindness: hereditary syndromes/disorders (CHARGE syndrome, Usher’s syndrome, Down’s syndrome), diseases that occurred before childbirth (cytomegalovirus, hydrocephalus, microcephaly), etc. The article presents a clinical case of an 11-year-old patient with a diagnosis of severe bilateral sensorineural hearing loss, condition after cochlear implantation on the right in 2012. Retinopathy of prematurity of the 5th degree, total retinal detachment with severe intraretinal proliferation. Infantile cerebral palsy. Hyperhomocysteinemia. Mitochondrial dysfunction. Casein intolerance. Persistent viral infection of Herpes Simplex Virus (HSV) type 6, Epstein–Barr virus (EBV). The authors showed a method for fitting the cochlear implant (CI) processor in a deaf-blind child by assessing the thresholds for perceiving sounds at different speech frequencies (500 Hz–4,000 Hz), which is the registration via Auditory Steady State Response (ASSR) to acoustic stimuli delivered through loudspeakers to an activated cochlear implant processor.

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The rationale for the use of three-phase stimulation for programming the processor of the cochlear implantation system (CI) in patients with deafness is presented. To study the possibilities of using a new type of stimulation, we selected patients with deafness after cochlear implantation, in whom signs of facial nerve stimulation (FNS) were established in the postoperative period. All subjects were previously installed in the CI processor with individual listening maps based on traditional biphasic stimulation. The use of three-phase stimulation to prevent SOS phenomena is caused by the geometry of the electric current pulse, which allows to reduce the penetrating power of the charge in the tissues and eliminate the effect on the facial nerve, without resorting to reducing the levels of stimulation necessary to create a dynamic range of sound perception. Comparative data of the parameters and the results of audiological testing in 21 patients with symptoms of SLE with traditional (two-phase) and three-phase electrical impulses in the stimulation algorithm of the CI system are presented. The positive effect of three-phase stimulation has been established. The results of the study show a significant increase in sound perception indicators when switching to a three-phase stimulation algorithm.