OBJECTIVES: Skin disorders are one of the main causes of medical consultation during childhood and its prevalence is highly influenced by environmental, genetic, and socioeconomic factors. In this study, we aimed to evaluate the epidemiological profile of pediatric patients attended at a dermatology referral service located in Amazon region, northern Brazil. METHODS: We retrospectively reviewed the medical history data of 638 pediatric patients (aged 0-15 years) presented at a dermatology referral service, between January 2014 and December 2019. The following variables were collected: gender, area of residence (urban or rural), diagnosis, date (year) of diagnosis, and comorbidities. Dermatoses were confirmed based on the available information of the patients’ detailed history, clinical presentation, and additional medical exams. RESULTS: A total of 831 diagnoses were included since 182 (28.52%) children had more than one dermatosis. The average age was 7.7 years, and the male-to-female ratio was 1: 0.94. The five most common categories of skin disorders were eczemas (29.72%), fungal infections (10.83%), tumors (9.51%), pigmentary disorders (8.90%), and urticaria/pruritus/drug eruptions (6.26%). Atopic dermatitis was the most reported disease, accounting for 18.41% of all diagnoses. The proportions of most dermatological conditions did not statistically differ between gender, except for pigmentary disorders that were significantly higher in female patients (p=0.01). CONCLUSIONS: Eczemas, fungal infections, and tumors were the most common groups of skin disorders among the evaluated children. However, more studies are needed to improve these data from northern Brazil.