Endometriosis is defined by the presence of endometrial tissues outside of the endometrial cavity. It is a benign condition and even though it's pathogenesis is not yet fully understood different theories, such as the Coelomic theory and the theory of Mullerian rest, have been proposed as possible explanations for the development of this pathology. Evidence suggests that women diagnosed with endometriosis presents an increased risk for developing ovarian cancers. Therefore, this review will explore the pathogensis of endometriosis, explore its association with the development of ovarian cancers and identify treatment methods for managing lesions following malignant transformation.