HighlightsSoft tissue sarcoma accounts for less than 1% of all malignant tumors.Early diagnosis of Retroperitoneal Liposarcoma is extremely difficult due to its location and early onset lack of symptoms.Complete surgical excision remains the mainstay of treatment.Complete resection of invaded organs must be weighed for its recurrence or patient adversity.Retroperitoneal Liposarcoma of well-differentiated subtypes has a good prognosis and low metastatic potential.

Endometrial Stromal Sarcomas are rare malignant tumours of the uterus. We report the case of incidental finding of Low-Grade Endometrial Stromal Sarcoma (LGESS) that metastasized to the retroperitoneum 14 years after the original surgery in a 72-year-old woman. The patient underwent a laparotomy and excision of all tumour nodules. Considering the common recurrence of and slow growing nature of LGESS, appropriate treatment options like surgical excision and life-long follow up should be considered.