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No abstract

The patient is a 27-year-old man with a constellation of symptoms including progressive, moderate, unilateral sensorineural hearing loss (SNHL) and tinnitus. Physical examination revealed a white patch of hair in the temporal region, one blue iris and one blue iris with a brown irridial patch that covered approximately 50% of the iris, no abnormalities of the medial canthii, and no pigmentary changes of the skin (Fig. 1). Audiograms done over a 5-year period showed progressive hearing loss during the previous 5 years on the left side. The head and neck examination was otherwise within normal limits, and the patient was healthy with a negative review of systems.