Sacro-coccygeal teratoma (SCT) is a type of tumor which mostly occurs in newborn babies. The vast majority of this type of tumor is benign. That pathology can be diagnosed antenatally or at birth. Teratomas, especially those diagnosed in the neonatal period, occur most frequently in the sacrococcygeal region. Clinically in many cases, we can observe a large swelling (mass) in the sacrococcygeal region. In some cases, there are signs of compression following by the displacement of the rectum and pelvic organs. Alphafetoprotein is the main biological test used. In association morphologically by echography, CT-scan, MRI and others, the tumor is classified. The classification used is the topographical one of TSCs, which was proposed by Altman to the American Academy of Pediatric Surgery. The mainstay of therapy is the complete surgical removal. We present a case of a newborn (6 months), female, with teratoma sacro-coccygeal. At birth the baby was noticed to have large swelling (mass), without any sign of compression of others organs. Clinical and paraclinical signs permitted us to conclude of a SCT type II of Altman's classification. A surgery was performed with a sacral approach. Histologically, tumors were classified into good (mature) category.