Hereditary haemorrhagic telangiectasia (HHT), also known as Osler–Weber–Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who presented with massive haemoptysis. Chest computed tomography scan was remarkable for a large anterior, left lower lobe arteriovenous malformation. The patient underwent a pulmonary angiogram with embolization of a large left lung arteriovenous malformation, which proved to be successful in controlling the bleeding.
Primary cardiac tumors are extremely rare. Incidence is approximately 0.017% of all primary tumors. Spindle cell sarcoma is the rarest, with only four cases reported and there are no guidelines for treating this condition. Cardiac sarcomas have symptoms by different mechanisms including obstruction, local invasion, and embolisms and in some cases the first manifestation could be a sudden cardiac death. Diagnosis is made with imaging techniques such as echocardiogram, cardiac computed tomography (CT), and magnetic resonance imaging (MRI) and confirmed with tissue biopsy. Patients with malignant tumors have a poor prognosis with an average mean survival of 6 months. Complete resection of the tumor remains the best treatment available. Spindle cell sarcoma may present with few symptoms and may remain silent until an advanced stage, thus limiting the few therapeutic options available.
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