Introduction:Christmas disease (Hemophilia B, factor IX hemophilia) is a rare bleeding disorder due to deficiency of coagulation factor IX 1 . Most commonly factor IX is quantitatively reduced, but in one-third of cases an abnormally functioning molecule is immunologically present. Factor IX deficiency is one-seventh as common as factor VIII deficiency hemophilia but is otherwise clinically and genetically identical.Factor IX deficiency or dysfunction occurs in 1 in 100,000 male births 2 . Accurate laboratory diagnosis is critical, since it is indistinguishable clinically from factor VIII deficiency (hemophilia A) but requires different treatment. Case Report:A 25 years old college student hailing from Mymenshing got himself admitted in BSMMU hospital on 2 nd February, 2009 with complaints of pain and restricted movement of left hip joint for 10 days, recurrent swelling and pain in multiple joint for last 20 years and prolonged bleeding following minor trauma since childhood.On examination patient is mildly anaemic, non icteric, pulse-92/min, BP-110/70 mm of Hg, no edema or lymphadenopathy. On examination of musculoskeletal system, there was wasting of thigh and calf muscles, tone was normal, power was 4/5, movement was reduced in both knee & elbow joints, as well as left hip joint. Nervous system and other system examination reveled nothing abnormal. Christmas Disease (Hemophilia -B) - Abstract:We report a 25 years old man developed Haemarthrosis of left hip joint with a history of recurrent swelling and pain in multiple joints and prolonged bleeding following minor trauma since childhood. Subsequent investigations revealed Christmas disease (Haemophilia B). Hemophilia B is an X-linked bleeding disorder. This case emphasises the importance of considering a diagnosis of haemophilia in a man with unexplained bleeding, even in the absence of a positive family history.[ BSMMU J 2009; 2(2): 90-91]

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