Introduction: Chordoma is a malignant neoplasm that arises from notochord remnants. Its incidence is highest above the age of 50 and behaves as a locally aggressive tumor with a slow growth rate. In most cases, complete surgical resection followed by radiotherapy offers the best chance of control. Developing metachronous tumors or distant metastasis is uncommon. Case Report: A 56-year-old male patient of sacral chordoma was treated by surgery and radiotherapy. He developed later bilateral inguinal lymph node metastasis and metachronous clivus chordoma. Conclusion: Chordomas are rare. Multiplicity of primary disease and distant metastasis could happen, so regular follow-up is warranted and more effective therapeutic modalities are needed. Keywords: Chordoma, sacrococcygeal tumors, notochord tumors, lymph node metastasis, clivus tumors.