The benign fibrous histiocytoma or fibrohistiocytoma is a benign neoplasm involving fibroblasts and histiocytes. The tumor occurs most often in the skin of the extremities, rarely commits deep soft tissues and parenchymal organs. The diagnosis can be very difficult and is histologically confirmed only. We present a case of a male patient of 14 months old, who presents with ascites due an unresectable benign fibrous histiocytoma. Was managed with four cycles of chemotherapy ARST protocol without evidence of improvement.