Highlights EPIDEMIOLOGY : paraganglioma of the ZUCKERKANDL organ is a rare neuroendocrine tumour but must be known. DIAGNOSIS : The typical presentation which is the Menard Triad of symptoms, associating headaches, sweating and palpitation. Preoperative diagnosis can be difficult in pauci-symptomatic cases. The Clinical signs, Abdominal-pelvic CT scan and biology are the steps of the preoperative diagnosis. TREATMENT : Treatment is surgical. Preoperative medical preparation is aimed at reducing risks of peroperative hemodynamic instability. The anesthetist should therefore prepare himself to manage blood pressure peaks during the tumour’s dissection, but also the possible low blood pressure at the end of exeresis. Surgery remains the key element of treatment and consists in exeresis of the paragaglioma. PROGNOSIS : paraganglioma of the ZUCKERKANDL organ is often a benign tumor. The resuscitation determines the patient’s prognosis.
BackgroundDermatofibrosarcoma protuberans is a rare tumor, representing about 0.1% of skin malignant tumors. It is characterized by local aggressiveness with significant potential for recurrence. Although metastasis is rare, it does occur. We report a case of a Burkinabe woman with dermatofibrosarcoma protuberans.Case presentationA 27-year-old Burkinabe woman consulted our institution for a recurrent scalp nodule that had been evolving for 13 years. At clinical examination, she was in good condition with a dry cough. An atrophic scarring alopecic plaque of 15-cm diameter in the right parietal region of the scalp, topped by an erythematous firm nodule measuring 3 × 2 × 2 cm, was noted, as well as a mobile nodule located in the axillary tail of the right breast. Cerebral computed tomodensitometry had not objectified the reach of the vault or the brain. A thoracic scan revealed four intrathoracic tissue masses straight to pleural touch. There were no evolutionary lesions in the abdominopelvic region. Histopathologic examination of the biopsy of the scalp nodule showed a proliferation of fibrous background, with fusiform cells carrying a storiform appearance. These cells had dark, elongated nuclei and showed some mitosis without atypia. The cells expressed CD34 intensely and diffusely. The test results were negative for PS100 and smooth muscle actin. The breast nodule showed the same profile as the scalp nodule.ConclusionsWe concluded on the diagnosis of scalp dermatofibrosarcoma protuberans with breast metastasis and probable pleuropulmonary metastasis.
Highlights Epidemiology: Lipoma of the mesocolon is a rare tumour less described in the literature. Diagnosis: It generally involves large masses. Clinically, it is often asymptomatic. When they exist, these symptoms are less specific and generally due to the large size of the tumour (compression, invagination, hernia). Imaging, especially TDM and MRI are an important step of the preoperative diagnosis. In imaging as in anatomopathology, lipoma-like liposarcoma is the main differential diagnosis. A differential diagnosis with lipoma-like sarcoma must be done. Treatment: Treatment is surgical. However, there are variations in the surgical procedures. Some authors had carried out lumpectomy. In our case, we carried out a left colectomy removing the tumour and the mesocolon, as well as the satellite lymph nodes. Each approach has its arguments, i.e. a conserving treatment exposing to repetition if the histological and/or immunochemistry data come out less reassuring, and a more secure and less invasive treatment. There is no consensus on the procedure which depends on the teams.
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