Desmoid tumours are rare; they account for about 0.03 percent of all neoplasms and less than 3 percent of all soft tissue tumours. The estimated incidence in the general population is two to four per million population per year. Here reporting a case of a 34-year-old female presenting with pain abdomen and swelling chest, excised mass diagnosed to be a desmoid tumour. KEYWORDSDesmoid Tumour. HOW TO CITE THIS ARTICLE: Philip AJ, Manoharan P, Ravy N. A case of desmoid tumour -abdominal fibromatosis in a young female, presenting with abdominal pain.