Background: Encephaloceles result from failure of the surface ectoderm to separate from the neuroectoderm. We aimed to review the data of cases with occipital encephalocele.

Arch Dis Child 2012;97(Suppl 2):A1-A539 A167 Abstracts months. Localised scrotal skin breakdown noted on day 11 with a rapidly progressive inflammation, necrosis and gangrene skin subcutaneous tissues. Regular dressing with duoderm, supportive care and I.V antibiotic has resolved necrotising fascitis with residual scar.Abstract 576 Figure 1 Conclusion We report the first case in literature of Genital Necrotising Fascitis in premature baby with Group B Streptococcus sepsis and meninigitis. It is relatively rare and has a fulminant course with a high mortality rate. We had good result with I.V antibiotic, supportive care and conservative surgical management. An encephalocele results from failure of the surface ectoderm to separate from the neuroectoderm. The prevalance ranges from 0.8 to 4 per 10.000 live births. The occiput is the most common site. During a 3 years' period 5 babies with occipital encephalocele were evaluated. All babies were girls. One mother was 45 years old, the others were around 25 years-old. All babies were born with cesarean sectio. Maternal folic acid (FA) consumption revealed that only 2 mothers used FA irregularly, not beginning preconceptionally. The 577 bilateral subdural collection. He was assessed at 10 month of age and found to have no residual disabilities. Conclusion VZV infection complicated by meningococcal sepsis and meningitis is well reported in the literature; subdural empyema is reported on few occasions; however we found no report with all these complications in a single patient nor in an infant. Psoas abscess is rare, especially in the neonatal period. It may be primary or rarely secondary to extend on from adjacent structures or to bacteremia caused by distant cutaneous infections. Vague clinical presentation may lead to delayed diagnosis. Appropriate drainage is necessary in addition to antibiotic therapy. Here we present a neonate was admitted with subcutaneous abscesses on his wrist and ankle. Staphylococcus aureus was isolated from the drainage material and proper antibiotic treatment was begun. On the 7 th day of treatment, he developed swelling on his groin and limited hip motion. Septic arthritis was suspected and a magnetic resonance imaging performed revealing an abscess on the right psoas muscle. Drainage and antibiotic treatment led to resolution of abscess. Development of multiple subcutaneous and deep abscesses in newborn period led us to suspect of primary immunodeficiency. In the immunological work up, serum immunoglobulins and lymphocyte sub set analysis were in normal ranges according to age. The phagocytic cell functions were tested with nitroblue-tetrazolium (NBT) slide test were also normal. Flow cytometry analyses revealed CD18 16%, CD11a + CD18 17%, CD11b + CD18 3%, CD11c + CD18 4%. A ratio of 1.89 oxidative explosion, 1.63 phagocytosis and 1.43 chemotaxis (N: >1.5) was determined in neutrophil function tests. Antibiotic prophylaxis was initiated and bone marrow transplantation was recommended. As a conclusion, immunodeficiency syndromes such as LAD...