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Congenital lobar emphysema is a very rare congenital cystic malformation of the lung that can cause acute respiratory distress early in life. This study reviews 19 cases of CLE over a period of 5 years at a Tertiary Pediatric Referral Center. The cases were studied with special emphasis on Histopathological findings of the lobectomy specimens, particularly bronchial cartilage abnormalties, radial alveolar count and their predictive value in pathogenesis of CLE. This condition can mimick other causes of respiratory distress in the neonatal period. Early diagnosis and effective surgical management is curatve.

Glial heterotopias are rare, benign, congenital, midline, non-teratomatous extra cranial glial tissues. They may masquerade as encephalocoele or dermoid cyst and mostly present in and around the nose. Clinically, these masses are firm and incompressible. Histologically, they are made up of astrocytes and neuroglial cells, embedded in fibrous and vascular connective tissue. Here in, we present 4 cases of nasal glial heterotopias. The first case was an 8 month old boy who presented with broadening of nose since birth. The second case was of 6 months old girl who presented with a soft tissue swelling over the root of the nose. The third case was of a 2 months old boy who presented with a soft tissue swelling over the nasolabial fold. The fourth case was a 5 month old boy with mass in left nostril. The radiological and histological features along with differential diagnosis are discussed. These cases are presented because of their rarity.

Ovarian tumors are rare in children and constitute 1% of all childhood malignancies and 8% of abdominal tumors. Large cysts and those complicated by torsion make their presence clear by their symptomatology. However, ovarian pathology is still mostly discovered at laparotomy for presumptive appendicitis. Accurate diagnosis of these tumors at such a young age is a great challenge to surgeons and pathologists. This article reviews the clinical presentation, radiological imaging, gross and histopathological findings at the Pathology Department of a Paediatric Referral centre in Hyderabad KEY WORDS: Ovarian tumors, pediatric age group, neoplastic, non-neoplastic lesions, germ cell tumors, surface-epithelial tumors, sex cord tumors. INTRODUCTION: Ovarian tumors are rare in children and constitute 1% of all childhood malignancies and 8% of abdominal tumors. Moreover, 10 to 30% of ovarian neoplasm operated during childhood or adolescent girls are malignant. It is well-known that germ-cell tumors are the commonest ovarian neoplasm in the first two decades of life constituting approximately two-thirds of all ovarian tumors. Malignant germ cell tumors constitute one-third of germ cell origin tumors and two-thirds of all ovarian malignancy in this age-group (1) Norris and Jensen found that <1% of epithelial carcinoma occurs below 20 years of age (2). Sex cord stromal tumors are rare tumors accounting for 5%-8% of all ovarian malignancies (3). Granulosa cell tumors are found in pre pubertal girls in