BACKGROUND Proliferative myositis is a rare benign tumor that is typically self-limiting and does not become malignant. It can be cured by simple resection without reported recurrence. Due to its rapid growth, hard structure and ill-defined borders, it can however be mistaken for malignant tumors such as sarcomas. CASE SUMMARY We investigate the case of a 64-year-old male with proliferative myositis of the abdominal wall, who was preoperatively administered a needle aspiration biopsy and given a simple excision and patch repair. We then compared it with other similar cases to determine the effectiveness of this treatment method. CONCLUSION Resection with follow-up observation has shown to be an effective treatment method for proliferative myositis. To avoid unnecessarily extended or destructive resection, a thorough and conclusive diagnosis is crucial, which requires adequate imaging and pathological knowledge.