No abstract

Pulmonary sequestration and congenital cystic adenomatous malformations (CCAM) are well known but still uncommon anomalies of the lung. Extralobar sequestrations are well described in association with CCAM, but fewer intralobar lesions are found with this association. The existence of striated muscle within CCAM is described, and we have evidence of dysplastic changes within the various cellular components occurring, with rhabdomyomatous dysplasia being one of these. A literature review shows no previous evidence of a reported intralobar sequestration associated with CCAM and rhabdomyomatous dysplastic changes.

Congenital mesoblastic nephroma (CMN) is a well-recognised renal tumour presenting in infancy, which has an excellent prognosis if completely excised. We describe the imaging appearances of an unusual, predominantly perinephric cystic CMN, with relative renal preservation but with retroperitoneal extension and bowel infiltration, which was complicated by hepatic metastases. To our knowledge, neither the appearance of the primary tumour nor the subsequent development of hepatic metastases has previously been reported. This appearance may represent a poor prognostic indicator for outcome. However, following partial hepatectomy, the patient remains disease-free at 1 year.