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Myoepithelial tumors are rare neoplasms that develop from myoepithelial cells in glandular structures and soft tissues. Primary intracranial myoepithelial neoplasms are even rarer with around ten cases reported. On the other hand, adrenocortical carcinoma (ACC) is also uncommon with an annual incidence of 0.7–2 per million and carries a poor prognosis. It is known to have an association with certain familial cancer syndromes. Even in sporadic cases, a significant portion of them had other malignancies before and after diagnosis of ACC. We reported a 34-year-old gentleman who was diagnosed to have ACC without known familial cancer syndrome. After that, he was also found to have right occipital myoepithelioma that was confirmed by excisional biopsy. There was no known association between these two pathologies. This is the first report of coincidence of ACC and intracranial myoepithelioma.

Primary cutaneous mucoepidermoid carcinoma (MEC) is a rare disease entity. Only around 20 cases have been reported so far. Herein, we present two cases for better understanding of the condition: A 74-year-old lady with a low-grade primary cutaneous MEC at her right external auditory ear canal was treated with surgical resection and adjuvant radiotherapy. The patient developed recurrence five months later and succumbed. Another 81-year-old lady with a high-grade primary cutaneous MEC carcinoma on her left parietal scalp treated by excisional biopsy remained disease free for 10 years. Their histological slides were discussed in details. Current evidence in the literature was also reviewed and summarized.