коллатеральных артерий на уровне легочного сегмента, играющих важную роль в определении тактики и объема хирургического лечения детей с атрезией легочной артерии с дефектом межжелудочковой перегородки 3-4 типов. По этой причине у этой группы пациентов АКГ остается методом выбора предоперационного планирования коррекции атрезии легочной артерии с дефектом межжелудочковой перегородки.

urpose. Demonstration of modern imaging modalities possibilities in the diagnosis and surgical correction planning of a rare combined congenital heart disease (CHD) in a newborn. Materials and methods. The article presents a clinical case of patient B., 1 day old, with prenatally suspected complex CHD. Patient was admitted to the intensive care department with signs of decreased saturation. For surgical management of CHD, the patient underwent transthoracic echocardiography (TTE) and CT-angiography (CTA) of heart and cardiac angiography.Results. On TTE ductus-dependent CHD, atresia of the pulmonary artery and the absence of interventricular and atrial septa were determined. In the preoperative planning the patient underwent a CTA of the heart and cardiac angiography for a detailed assessment of the pulmonary arteries and patent ductus arteriosus (PDA) anatomy. Identifying possible anomalies of the pulmonary veins and aortopulmonary collaterals was important to determine the surgical tactics.Discussion. TTE has high diagnostic quality in the diagnosis of combined CHD with the pulmonary artery atresia, however, it cannot be considered as a final diagnostic step in surgical correction planning due to limitations in the visualization of extracardiac anomalies. Conclusion.Multimodal diagnostic approach for assessing various anatomical and functional parameters of the heart and extracardiac structures should be used in all children with complex, combined CHD.

urpose. To assess the role of trans-thoracic echocardiography (TTE), CT-angiography (CTA) and cardio-MRI in the routine evaluation of aortic coarctation (CoAo) and preoperative planning in children. Materials and methods.The study comprised 119 patients -all of them underwent TTE, 101 -CTA, 41 -underwent cardio-MRI. On TTE, CTA and cardio-MRI aorta morphometry was performed. All important intra-and extracardiac findings were assessed.Results. The diagnostic accuracy of the TTE, CTA and cardio-MRI was 88.2%, 96.3% and 90.2% respectively. The preoperative accuracy of TTE was inferior to CT methods in determining the pathology of brachiocephalic vessels, aberrant right subclavian artery and vascular collaterals: 36%, 7%, 13%, respectively. CTA is more accurate in determining extracardiac anomalies compared to TTE. The diagnostic accuracy of CTA in determining the pathology of brachiocephalic vessels, aberrant right subclavian artery and vascular collaterals was: 100%, 100% and 87% respectively. In determining septal defects, TTE was more effective in comparison with CTA, the diagnostic accuracy of the technique was 96% against the result of CTA in 87%.Conclusion. TTE is a screening method and has a high diagnostic value in determining aortic coarctation, however, it cannot be final and preferable in pre-surgical planning due to limited visualization of extracardiac anomalies. CT methods are highly effective both in determining the pathology of the aortic arch and in identifying concomitant anomalies. Because of the technical limitations and difficulties in conducting MRI of the heart in younger children, the lack of additional significant information in comparison with CTA of the heart, cardio-MRI is not the method of choice in the diagnosis of CoAo in young children. For older children, cardio-MRI is an alternative to CTA in the diagnosis and preoperative planning of CoAo.