Cavernous haemangioma is a slow-growing benign vascular tumor. It arises most frequently from the vertebral bodies or bones of the skull and face, the main affected being the frontal bone, the parietal bone, the orbital bone, the zygoma, maxilla, the mandible and nasal bones. Cavernous haemangioma of the nasal pyramid is very rare. In this review, we discuss the most important characteristics of this rare tumor, while presenting the clinical case of a 15-year-old male patient diagnosed in 2012 with a tumor located in the bones of the nasal pyramid, which turned out to be a cavernous haemangioma. The patient came to our clinic for swelling of the nasal pyramid with overlying skin of normal aspect, which appeared about 4 years before, with progressive evolution. The clinical examination showed a round-oval tumor with approximately 3/3 cm in diameter, hard, painless, without inflammatory signs, located in the region of the nasal pyramid, developed especially on the left side. The surgical treatment consisted in complete removal of the tumor through external approach, by lateral rhinotomy. There was no recurrence in the 10-year follow-up period. The particularity of this case is represented by the age and rare occurrence of cavernous haemangioma in the bones of the face, especially at the level of the nasal pyramid. Complete resection of the tumor represents the “gold standard” treatment.