Aims To survey perioperative management practices for paediatric patients diagnosed with autism spectrum disorder (ASD). Methods A systematic review was carried out of empirical studies and case reports published in peerreviewed journals of current best practices and behavioural interventions for paediatric patients with ASD who had undergone surgery. Results The final sample included 11 articles published between 1997 and 2016 that met broad inclusion criteria of surveying perioperative interventions for the ASD population. There is broad endorsement across the scant publications on this topic of the following practices: increased attention to individual patient needs, rehearsal and other desensitisation efforts, departure from a sole focus on sedation or restraint of the combative or uncooperative patient and engaging caregivers in tuning perioperative management to individual needs. Conclusions This review supports the need for an individualised structure and approach to the perioperative care of these unique patients.