<p class="abstract">Choanal polyp arising from the sphenoid sinus and presenting at the choana are rare. These are known as sphenochoanal polyp. We present a case of sphenochoanal polyp and its clinical features and surgical management is discussed. Our aim in this case was to properly delineate the origin of the polyp and differentiate it from other lesions such as the antrochoanal polyp and meningocele, followed by meticulous endoscopic excision of the polyp. Radiological investigations include a CT scan paranasal sinuses or a MRI diagnostic nasal endoscopy will confirm the diagnosis. Once the diagnosis is made surgical removal must be done<span lang="EN-IN">.</span></p>

<p class="abstract">We report a case of sixth nerve palsy as a rare complication of acute otitis media (apical petrositis). The clinical triad of symptoms consisting of retro-orbital unilateral pain related to trigeminal nerve involvement, diplopia due to sixth nerve palsy and persistent otorrhea is known as Gradenigo syndrome. The patient was treated with intravenous antibiotics along with modified radical mastoidectomy and had complete resolution of his symptoms.</p>

<p class="abstract"><span lang="EN-IN">Hajdu Cheney syndrome is extremely rare autosomal dominant congenital disorder of connective tissue. It may occur due to spontaneous de novo mutation and mutation in NOTCH-2 gene identified recently. Most characteristic features include aero-osteolysis involving phalanges of both hands and feet, osteoporosis, deformities of skull, mandible, spine and other bones, kyphoscoliosis and bone fractures. Rarely in some affected individuals, it causes joint hypermobility, dental problems, hearing loss, heart defects, kidney abnormality like polycystic kidneys, excess body hair and recurrent infections in childhood. It affects many parts of body particularly bones. Treatment is symptomatic. In this case report, we present a case of 14 years male child with features of Hajdu Cheney syndrome with genetic predisposition. Patient presented to ENT clinic with complaint of hearing loss.</span></p>