PURPOSE:To report a case of Central Macular Areolar Dystrophy and to discuss the literature pertaining to it. METHODS: Clinical data including medical history, findings on physical examination and local examination were recorded for a 35years old male, case of Central Macular Areolar Dystrophy. No treatment was advised and patient was called for regular follow up to cater for low vision aids if required in the future. RESULTS: Best corrected Visual acuity of the patient remained constant at 6/36 for a period of one year with the patient being on 3monthly follow up. CONCLUSION: No particular or specific treatment is available for this rare macular dystrophy. The only modality available in the form of low vision aids for progressive disease.