No abstract

Patients with mesenteric fibromatosis (MF) are clinically asymptomatic, with little or no focal symptoms until later in their course, at which time they complain of pain, abdominal discomfort, constipation, vomiting, abdominal mass, weight loss, and symptoms due to organ compression. Generally, it occurs as an abdominal mass but may also present in many different ways. In some cases, trauma, previous abdominal surgery, and hormonal stimulation (such as estrogen) may play a role in onset of this neoplasm. Patients with Mayer-Rokitansky-Kuster-Hauser syndrome present primary amenorrhea and may have some other anomalies, including hearing defects, heart defects, skeletal deformities, and genital neoplastic diseases. We diagnosed duodenal obstruction due to MF in a patient with type I Mayer-Rokitansky-Kuster-Hauser syndrome.

A 23-year-old male patient who presented with impaired kidney function tests attended to hospital for hemodialysis and underwent 18 F-FDG positron emission tomography/computed tomography (PET/CT) examination for the metabolic characterization of the intra-abdominal mass which was found in the ultrasonography. 18 F-FDG PET/CT revealed a mass lesion adjacent to the liver which was hypermetabolic and the pathology of the lesion was determined as amyloidosis. To the best of our knowledge, the case with 18 F-FDG PET/CT images of a huge amyloid mass is the first in the literature. AbstractYirmi üç yaşında erkek hasta böbrek yetmezliği ile diyaliz için hastanemize yönlendirilmiştir. Hastanın ultrasonografisinde tesadüfen saptanan intra-abdominal kitle lezyonunun metabolik karakterizasyonu için yapılan 18 F-FDG pozitron emisyon tomografi/bilgisayarlı tomografi (PET/BT) çalışmasında hipermetabolik kitle izlenmiş olup kitlenin biyopsisi amiloidozis ile uyumlu olarak bulunmuştur. Bilgilerimize göre, bu olgu ile, dev amiloid kitlesi ile başvuran bir hastanın 18 F-FDG PET/BT görüntüleri literatürde ilk kez sunulmaktadır. Anahtar kelimeler: Amiloidoz, abdominal kitle, 18 F-FDG pozitron emisyon tomografi/bilgisayarlı tomografi Öz