Background: Inherited epidermolysis bullosa (EB) is a genetic disorder characterized by skin fragility and unique oral features. Aims: To provide (a) a complete review of the oral manifestations in those living with each type of inherited EB, (b) the current best practices for managing oral health care of people living with EB, (c) the current best practices on dental implant-based oral rehabilitation for patients with recessive dystrophic EB (RDEB), and (d) the current best practice for managing local anesthesia, This is an open access article under the terms of the Creative Commons Attribution License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.

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The association with use of fluoride tablets and varnish probably reflects reverse causality but indicates the need for early preventative interventions in children with UCLP.

Factors increasing the risk of hospital admission among cleft children should be taken into account when planning services. Efforts to reduce the number of hospital admissions should be focused on disease prevention, particularly among those most at risk of caries.

A positive association was established between dental decay and the presence of a fistula. Although not proven as causative, possible reasons for this include nasal mucus retaining sugary food in the mouth and an overall prolonged food-clearance time. The known association between severity of cleft and an increased likelihood of a fistula and severity of cleft and increased dental decay were again demonstrated but were not found to be the exclusive explanation for the new finding of an association between fistulae and higher dental decay rates.